Diffuse cutaneous involvement and sinus histiocytosis with massive lymphadenopathy.
نویسندگان
چکیده
Severe skin involvement complicated a case of sinus histiocytosis with massive lymphadenopathy in a young Malay girl. The clinical and histological features of this rare manifestation are described.
منابع مشابه
Extranodal Rosai-Dorfman Disease with Cutaneous and Periodontal Involvement: A Rare Presentation
Sinus histiocytosis with massive lymphadenopathy (SHML) or Rosai-Dorfman disease (RDD) was first described as a distinct clinicopathological entity by Rosai and Dorfman in 1969. SHML is commonly characterized by painless cervical lymphadenopathy, and its clinical course is generally benign and self-limiting. This disorder commonly involves the lymph nodes but may secondarily involve the skin. H...
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ESR: erythrocyte sedimentation rate INTRODUCTION Rosai-Dorfman disease, also called sinus histiocytosis with massive lymphadenopathy, is a rare histiocytic condition of unknown etiology first described in 1969. Primary cutaneous manifestation without systemic involvement of Rosai-Dorfman disease is even more uncommon. Here we present a case of primary cutaneous manifestation of Rosai-Dorfman di...
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متن کاملRosai-Dorfman disease presenting with isolated bilateral orbital masses: report of two cases.
Rosai-Dorfman disease (sinus histiocytosis with massive lymphadenopathy) is a rare benign idiopathic proliferative disease of phagocytic histiocytes. Approximately 80% of patients present with painless massive cervical lymphadenopathy. Isolated extranodal involvement is relatively uncommon. Two cases of Rosai-Dorfman disease are reported: one with isolated bilateral orbital involvement and one ...
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عنوان ژورنال:
- Postgraduate medical journal
دوره 56 657 شماره
صفحات -
تاریخ انتشار 1980